Dermatofibrosarcoma protuberans (DFSP) is a rare neoplasm of the dermis layer of the skin, and is classified as a sarcoma. In many respects, the disease behaves as a benign tumor, but in 2-5% of cases it can metastasize, so it should be considered to have malignant potential.
Dermatofibrosarcomaprotuberans is a fibrohistiocytic tumour of intermediate malignancy,characterized by a distinctive storiform growth pattern and frequent local recurrences.
Dermatofibrosarcomaprotuberans with fibrosarcomatous areas: a clinico-pathologic and immunohistochemic study in four cases.
Dermatofibrosarcomaprotuberans, giant cell fibroblastoma, and hybrid lesions in children: clinicopathologic comparative analysis of 28 cases with molecular data--a study from the French Federation of Cancer Centers Sarcoma Group.
Dermatofibrosarcomaprotuberans is genetically characterized by the unbalanced chromosomal t(17;22)(q21;q13), usually in the form of a supernumerary ring chromosome.
Dermatofibrosarcomaprotuberans (DFSP) is a dermal and subcutaneous tumor categorized as a tumor of intermediate malignancy, and its progression in some cases to fibrosarcoma is well known.
Dermatofibrosarcomaprotuberans (DFSP) is a fibrohistiocytic tumor of intermediate malignancy characterized by a distinctive storiform growth pattern and frequent local recurrences.