DEFINITION
Total for all ages and sexes. Database compiled January 2004. Total of figures for:
- Disorders of sphingolipid metabolism and other lipid storage disorders
- GM2 gangliosidosis
- Other gangliosidosis
- Other sphingolipidosis
- Sphingolipido Per capita figures expressed per 1 million population.
| Rank |
Countries
|
Amount
|
|
# 1
|
Iceland: |
6.73997 deaths per 1 million peo |
|
|
# 2
|
Bahamas, The: |
3.31356 deaths per 1 million peo |
|
|
# 3
|
Bahrain: |
2.90552 deaths per 1 million peo |
|
|
# 4
|
Malta: |
2.5092 deaths per 1 million peo |
|
|
# 5
|
Israel: |
2.38968 deaths per 1 million peo |
|
|
# 6
|
Luxembourg: |
2.13415 deaths per 1 million peo |
|
|
# 7
|
Finland: |
1.72315 deaths per 1 million peo |
|
|
# 8
|
Chile: |
1.62693 deaths per 1 million peo |
|
|
# 9
|
Denmark: |
1.28866 deaths per 1 million peo |
|
|
# 10
|
Netherlands: |
1.03614 deaths per 1 million peo |
|
|
# 11
|
Sweden: |
0.999778 deaths per 1 million peo |
|
|
# 12
|
Costa Rica: |
0.996016 deaths per 1 million peo |
|
|
# 13
|
Canada: |
0.884012 deaths per 1 million peo |
|
|
# 14
|
Norway: |
0.87089 deaths per 1 million peo |
|
|
# 15
|
Kuwait: |
0.856164 deaths per 1 million peo |
|
|
# 16
|
Australia: |
0.846192 deaths per 1 million peo |
|
|
# 17
|
Argentina: |
0.758764 deaths per 1 million peo |
|
|
# 18
|
United States: |
0.639088 deaths per 1 million peo |
|
|
# 19
|
Austria: |
0.610874 deaths per 1 million peo |
|
|
# 20
|
Spain: |
0.57014 deaths per 1 million peo |
|
|
# 21
|
Slovenia: |
0.497265 deaths per 1 million peo |
|
|
# 22
|
New Zealand: |
0.495663 deaths per 1 million peo |
|
|
# 23
|
Germany: |
0.473123 deaths per 1 million peo |
|
|
# 24
|
Croatia: |
0.44484 deaths per 1 million peo |
|
|
# 25
|
Poland: |
0.440894 deaths per 1 million peo |
|
|
# 26
|
Latvia: |
0.436681 deaths per 1 million peo |
|
|
# 27
|
Czech Republic: |
0.390587 deaths per 1 million peo |
|
|
# 28
|
Panama: |
0.318471 deaths per 1 million peo |
|
|
# 29
|
Uruguay: |
0.29274 deaths per 1 million peo |
|
|
# 30
|
Lithuania: |
0.278009 deaths per 1 million peo |
|
|
# 31
|
Mexico: |
0.273062 deaths per 1 million peo |
|
|
# 32
|
Puerto Rico: |
0.255689 deaths per 1 million peo |
|
|
# 33
|
Venezuela: |
0.236453 deaths per 1 million peo |
|
|
# 34
|
Korea, South: |
0.226147 deaths per 1 million peo |
|
|
# 35
|
Moldova: |
0.224467 deaths per 1 million peo |
|
|
# 36
|
Colombia: |
0.209526 deaths per 1 million peo |
|
|
# 37
|
Brazil: |
0.193431 deaths per 1 million peo |
|
|
# 38
|
Slovakia: |
0.184128 deaths per 1 million peo |
|
|
# 39
|
Ecuador: |
0.149656 deaths per 1 million peo |
|
|
# 40
|
Japan: |
0.117724 deaths per 1 million peo |
|
|
# 41
|
South Africa: |
0.112755 deaths per 1 million peo |
|
|
# 42
|
Hungary: |
0.09993 deaths per 1 million peo |
|
|
# 43
|
Cuba: |
0.088129 deaths per 1 million peo |
|
|
# 44
|
United Kingdom: |
0.0496352 deaths per 1 million peo |
|
|
# 45
|
Romania: |
0.0447828 deaths per 1 million peo |
|
| |
Weighted average: |
0.9 deaths per 1 million peo |
|
DEFINITION: Total for all ages and sexes. Database compiled January 2004. Total of figures for:
- Disorders of sphingolipid metabolism and other lipid storage disorders
- GM2 gangliosidosis
- Other gangliosidosis
- Other sphingolipidosis
- Sphingolipido Per capita figures expressed per 1 million population.